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International Journal of Applied Research
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ISSN Print: 2394-7500, ISSN Online: 2394-5869, CODEN: IJARPF

IMPACT FACTOR (RJIF): 8.4

Vol. 8, Issue 1, Part A (2022)

Straatsma syndrome: Unilateral myelinated retinal nerve fiber layer, high myopia, strabismus and amblyopia: Case report

Straatsma syndrome: Unilateral myelinated retinal nerve fiber layer, high myopia, strabismus and amblyopia: Case report

Author(s)
Dr. P Thenmozhi and A Helen Vinitha
Abstract
Straatsma syndrome is a rare disease entity characterized by the traditional triad of unilateral myelinated retinal nerve fibers (MNRF), axial myopia, and amblyopia. The original description of the condition also included strabismus. Variations of the triad include a “reverse Straatsma syndrome”, in which patient’s exhibit hyperopic instead of myopia. Even though nystagmus and strabismus have not been prominently associated with Straatsma syndrome, either may be present as complimentary findings without precluding one from the diagnosis. A 12-year-old boy presented with report of decreased vision in the right eye for the last year. On examination, his best-corrected visual acuity was 1.78 log MAR in the right eye and 0 log MAR in the left eye. Cycloplegic retinoscopy revealed a refractive error of a −15 dioptre sphere with a −3.5 dioptre cylinder at 180° in the right eye. The patient had right exotropia of 10 prism diopters on modified Krimsky’s test with full extra ocular motility.
Pages: 31-32  |  442 Views  78 Downloads


International Journal of Applied Research
How to cite this article:
Dr. P Thenmozhi, A Helen Vinitha. Straatsma syndrome: Unilateral myelinated retinal nerve fiber layer, high myopia, strabismus and amblyopia: Case report. Int J Appl Res 2022;8(1):31-32.
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